Large aortic aneurysm and dissection in a patient with Marfan's syndrome

Autores

  • Fernando Pivatto Júnior Cardiology Division, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - Brazil Mailing address: Fernando Pivatto Júnior, MD Cardiology Division – Hospital de Clínicas de Porto Alegre Rua Ramiro Barcelos, 2350 Sala 2060 90035-903 – Porto Alegre, RS - Brazil E-mail: fpivatto@gmail.com Phone: +55 51 3359-8342
  • Leila Denise Cardoso Ramos Cardiology Division, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - Brazil
  • Murilo Foppa Cardiology Division, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - Brazil
  • Felipe Soares Torres Radiology Department, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - Brazil

Palavras-chave:

Marfan’s syndrome, aortic aneurysm, dissection

Resumo

Marfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive cardiac failure. In this report, we present a patient with a large symptomatic aortic aneurysm and chronic dissection, severe aortic regurgitation and cardiomegaly, treated successfully with resection of the proximal aorta and placement of a mechanic aortic valved graft. 

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Publicado

2015-04-28

Como Citar

1.
Pivatto Júnior F, Ramos LDC, Foppa M, Torres FS. Large aortic aneurysm and dissection in a patient with Marfan’s syndrome. Clin Biomed Res [Internet]. 28º de abril de 2015 [citado 8º de dezembro de 2022];35(2). Disponível em: https://www.seer.ufrgs.br/index.php/hcpa/article/view/52524

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